A healthy result should fall into the range 0 - 0.42 mmol/mol creatinine.
2-Hydroxyisovaleric acid (aka 2-Hydroxy-3-methylbutyric acid) is a branched-chain amino acid metabolite.
2-hydroxy-3-methylbutyric acid is a valine derivative that is valine in which the amino group has been replaced by a ‘hydroxy’ group.
insert the value from you 2-Hydroxyisovaleric test result.
Moderate increase may result from:
- lactic acidosis
- episodic ketosis
- thiamine/lipoic acid deficiency
Patients with slight to moderate elevations may use dietary supplements containing thiamine to improve clinical symptoms.
Significant elevations are associated with:
- A significant increase of branched-chain amino acid metabolites is associated with the genetic disorders, maple syrup urine disease (MSUD) and pyruvate dehydrogenase deficiency.
- Elevated levels have been linked to short bowel syndrome.
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2-Hydroxybutyric, 2-Hydroxyhippuric, 2-Hydroxyisocaproic, 2-Hydroxyisovaleric, 2-Hydroxyphenylacetic (female), 2-Oxo-4-methiolbutyric, 2-Oxoglutaric (female), 2-Oxoisocaproic, 2-Oxoisovaleric, 3-Hydroxy-3-methylglutaric (HMG), 3-Hydroxybutyric, 3-Hydroxyglutaric (female), 3-Indoleacetic (female), 3-Methyl-2-oxovaleric, 3-Methylglutaconic (female), 3-Methylglutaric (female), 3-Oxoglutaric (female), 4-Cresol (female), 4-Hydroxybenzoic (female), 4-Hydroxybutyric, 4-Hydroxyhippuric (female), 4-Hydroxyphenylacetic, 4-Hydroxyphenyllactic, 5-Hydroxyindoleacetic (5-HIAA), 5-Hydroxymethyl-2-furoic (female), Acetoacetic, Aconitic, Adipic, Arabinose (female), Ascorbic, Carboxycitric (female), Citramalic (female), Citric, DHPPA (Beneficial Bacteria) (female), Ethylmalonic, Fumaric (female), Furan-2,5-dicarboxylic (female), Furancarbonylglycine (female), Glutaric, Glyceric, Glycolic, Hippuric (female), Homogentisic, Homovanillic (HVA), HPHPA (female), HVA / VMA Ratio, Kynurenic, Lactic, Malic (female), Malonic, Mandelic, Methylcitric, Methylmalonic, Methylsuccinic, N-Acetylaspartic, N-Acetylcysteine (NAC), Orotic, Oxalic, Pantothenic (B5), Phenyllactic, Phenylpyruvic, Phosphoric, Pyridoxic (B6), Pyroglutamic, Pyruvic, Quinolinic, Quinolinic / 5-HIAA Ratio, Sebacic, Suberic, Succinic (female), Tartaric (female), Thymine, Tricarballylic (female), Uracil, Vanillylmandelic (VMA) (female)
